PICU Clinical Pathway for Evaluation/Treatment of Children with Jeune Syndrome/Chest Wall Hypoplasia Undergoing VEPTR Implantation
- Related Pathway
- VEPTR Procedures
Special Considerations
Hospital admission for Full Evaluation to Optimize Patient Status, Plan for Surgical Procedure & Post-operative Care
- Consults on Admission
- Preoperative Imaging
- Labs
- Refer to Jeune Syndrome Admission Order Set
Patient to OR for VEPTR Implantation
Intra-operative Management
Admit to PICU
Refer to IP Orthopaedic Jeune VEPTR Post Operative Management Order Set
- Goals:
- Maintain Analgesia
- Maintain Invasive Ventilatory Support
- Goals:
- Maintain Analgesia – Begin PO Pain Medication if Possible
- Mobilization
- Maintain Wound Integrity
- Assess Nutrition Readiness for Patients with Tracheostomy
- Consider Readiness for Extubation
- Goals:
- Wean from PCA
- Advance Nutrition
- Maintain Mobility
- Consider Readiness for Extubation
- Begin Education for Discharge
- Goals:
- Advance Nutrition
- Maintain Mobility
- Enteral Pain Management
- Goals:
- First Dressing Change
- Education for Managing Patient at Home
- Baseline Respiratory Status
Discharge Education for Orthopaedic Care
- Goals:
- Baseline Pulmonary Status
- Enteral Medication
- Tolerating Baseline Enteral Feeds
- Pass PT and OT Requirements
Posted: July 2019
Revised: June 2022
Authors: K. Devine, CRNP; L. McNeely, CRNP; J. Anari, MD; P. Cahill, MD; D. Davis, MD; O. Mayer, MD; I. Yuan, MD; A. Boyd, CRNP; D. Platenecky, DPT; J. Vicencio, DPT; L. Rhodes, RT; K. Semless, CRNP
Revised: June 2022
Authors: K. Devine, CRNP; L. McNeely, CRNP; J. Anari, MD; P. Cahill, MD; D. Davis, MD; O. Mayer, MD; I. Yuan, MD; A. Boyd, CRNP; D. Platenecky, DPT; J. Vicencio, DPT; L. Rhodes, RT; K. Semless, CRNP